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Volume 3,Issue 7

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20 May 2025

超声评估地中海贫血孕妇胎儿心脏功能的研究进展

少飘 陈1
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1 海南省人民医院, 中国
© 2025 by the Author. Licensee Art and Design, USA. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution -Noncommercial 4.0 International License (CC BY-NC 4.0) ( https://creativecommons.org/licenses/by-nc/4.0/ )
Abstract

地中海贫血是由于形成血红蛋白四聚体(α2β2)的α/β珠蛋白链的结构和合成异常所致,由于珠蛋白α链或β链合成量不足或缺失,血红蛋白形成障碍,红细胞的无效生成导致一系列临床症状出现,如慢性溶血性贫血、代偿性造血扩张、血凝过多和肠道铁吸收增加等。早期发现地中海贫血孕妇胎儿心脏功能异常能及时有效进行干预,对孕妇及胎儿具有重要的临床意义。超声是一种产前无创筛查的常用检查方法,可以判断胎儿宫内状态、评估其生长发育情况。通过超声检查进行产前筛查使早期发现胎儿心脏功能损害成为可能。本文就超声评估地中海贫血孕妇的胎儿心脏功能的研究进展,比较各种超声检查方法的优势和不足,为临床早期评估地中海贫血孕妇胎儿心脏功能提供更多的方法。

Keywords
地中海贫血
超声检查
胎儿心脏
References

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